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Congenital Short Bowel Syndrome with Malrotation.

Author(s): Shih-Ming Chu | Chih-Cheng Luo | Yi-Hong Chou | Ju-Bei Yen

Journal: Chang Gung Medical Journal
ISSN 2072-0939

Volume: 27;
Issue: 07;
Start page: 548;
Date: 2004;
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Keywords: short bowel syndrome | malrotation | parenteral nutrition | glutamine.

Congenital short bowel syndrome (SBS) associated with malrotation and malabsorptionis a very rare condition. We report on an infant girl with congenital SBS associated withmalrotation and malabsorption. No polyhydraminos was noted during the regular prenatalexamination. Protracted postnatal postprandial vomiting with progressive failure to thrivewas noted. A laparotomy showed the small bowel was only about 20 cm in length. Sheeventually survived with short-term parenteral nutrition and use of oral L-glutamine supplementation.To our knowledge, this might be the shortest length of bowel loop ever reported.Currently, she is 15 months of age with a body weight of about 7 kg and good development.
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