Academic Journals Database
Disseminating quality controlled scientific knowledge

ENUCLEATION IN A PATIENT WITH NEUROFIBROMATOSIS TYPE 1 WITH BUPHTHALMOS AND OCULAR DEFORMITY

ADD TO MY LIST
 
Author(s): F. Asadi-Amoli | A. Ariapad S. Z. Tabatabaei

Journal: Acta Medica Iranica
ISSN 0044-6025

Volume: 45;
Issue: 6;
Start page: 515;
Date: 2007;
Original page

Keywords: Neurofibromatosis-1 | plexiform neurofibroma | buphthalmos | enucleation

ABSTRACT
To report a case of buphthalmos with neurofibromatosis (NF-1) who suffered with blindness suffered enucleation. Physical examination & histopathology were performed. Physical examination revealed Buphthalmos & vascularized cornea with lower lid ectropion and orbital deformity. Histopathologic findings shows plexiform neurofibroma in orbital tissue with scleral wall involvement. And hamartomatous proliferation in choroid & cilliary bodies with melanocytic elements. Few NF-1 cases with buphthalmos have been reported. But cases with complicationg buphthalmos (retinal Detachment & optic nerve Atrophy) suffering enucleation are very rare.
Why do you need a reservation system?      Save time & money - Smart Internet Solutions