Author(s): Kumar B | Mutu R | Puri G | Singh Anju | Rana S
Journal: PVRI Review
ISSN 0974-6013
Volume: 2;
Issue: 3;
Start page: 126;
Date: 2010;
Original page
Keywords: pulmonary hypertension | Sildenafil | total anomalous pulmonary venous connection | vertican vein
ABSTRACT
We report a case of supracardiac total anomalous pulmonary venous connection (TAPVC) with persistent post operative pulmonary hypertension unresponsive to sildenafil. Only after ligation of vertical vein, echocardiography could detect a perimembranous ventricular septal defect (VSD). Following VSD closure, pulmonary artery pressure declined and patient improved.
Journal: PVRI Review
ISSN 0974-6013
Volume: 2;
Issue: 3;
Start page: 126;
Date: 2010;
Original page
Keywords: pulmonary hypertension | Sildenafil | total anomalous pulmonary venous connection | vertican vein
ABSTRACT
We report a case of supracardiac total anomalous pulmonary venous connection (TAPVC) with persistent post operative pulmonary hypertension unresponsive to sildenafil. Only after ligation of vertical vein, echocardiography could detect a perimembranous ventricular septal defect (VSD). Following VSD closure, pulmonary artery pressure declined and patient improved.