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Cardiac arrest after anesthetic management in a patient with hereditary sensory autonomic neuropathy type IV

Author(s): Ergül Yakup | Ekici Baris | Keskin Sabiha

Journal: Saudi Journal of Anaesthesia
ISSN 1658-354X

Volume: 5;
Issue: 1;
Start page: 93;
Date: 2011;
Original page

Keywords: Anhydrosis | cardiac arrest | hereditary sensory autonomic neuropathy type IV | hyperprexia | self mutilation

Hereditary sensory autonomic neuropathy type IV is a rare disorder with an autosomal recessive transmission and characterized by self-mutilation due to a lack in pain and heat sensation. Recurrent hyperpyrexia and anhydrosis are seen in patients as a result of a lack of sweat gland innervation. Self-mutilation and insensitivity to pain result in orthopedic complications and patients undergone recurrent surgical interventions with anesthesia. However, these patients are prone to perioperative complications such as hyperthermia, hypothermia, and cardiac complications like bradycardia and hypotension. We report a 5-year-old boy with hereditary sensory autonomic neuropathy type IV, developing hyperpyrexia and cardiac arrest after anesthesia.
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